China Dairy ›› 2022, Vol. 0 ›› Issue (10): 104-110.doi: 10.12377/1671-4393.22.10.19

• DAIRY INDUSTRY • Previous Articles    

Analysis of Dietary Nutrition Supplement in Children with Phenylketonuria

WANG Yancong   

  1. Qingdao Shengtong Nutritional Food Co.,Ltd.,Beijing Technology Center,Beijing 101100
  • Online:2022-10-25 Published:2022-11-11

Abstract: Phenylketuria(PKU)is an autosomal recessive disorder with abnormal metabolism,which can cause neurocognitive and neuromotor disorders,autistic behavior,eczema,epilepsy and other complications in children. In the course of treatment,while limiting diet through low Phe,it is also necessary to pay attention to the nutritional problems of other nutrients in children. Therefore,the development of formula powder with amino acid metabolic disorders for special medical purpose suitable for PKU children aged 1~10 years is of great significance to ensure the normal growth and development of children. In this paper,the classification of PKU,diet therapy and nutrient deficiency of PKU children were reviewed,focusing on the analysis of low protein diet,formula powder with amino acid metabolic disorders for special medical purpose based on free amino acids and the lack and supplement of some nutrients in PKU children,in order to provide theoretical guidance and reference for the nutrition problems in PKU diet therapy and the development of formula powder with amino acid metabolic disorders for special medical purpose.

Key words: phenylketonuria, dietotherapy, formula powder with amino acid metabolic disorders for special medical purpose, nutrients

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